Recently, a benign variant of scleroderma, called the C.R.S.T. syndrome, has been described by Winterbauer.
Patients with this disorder have skin changes such as dermal and subcutaneous calcinosis, Raynaud´s phenomenon, sclerodactyly, and telangiectasia.
With the passible exception of the gastrointestinal system, involvement of other organs is uncommon, and affected individuals have a long clinical course.
A case of C.R.S.T. syndrome in 25-year-old female in reported with brief review of literatures. The patient showed multiple pea sized nodular deposits on dermal and subcutaneous layers of both elbow and knee joints, Raynaud´s phenomenon, sclerodactyly with acrosclerosis and sclerodermatous change on both hands and forearm and tela.ngiectasia on face and both palms.
On esophagogram, slight disturbance of passage at the cardioesophageal junction area was noted.
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